Õý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«

ÓÐÎʱشð

ËÑË÷´ð°¸

ÓÐÎʱشð > ÄÚ¿Æ > ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡

¦Á1¿¹Òȵ°°×øȱ

¦Á1¿¹Òȵ°°×øȱ·¦ÐÔ

|Óû§¹Ø×¢¶È£º

ÖÜ0% ÔÂ0%
1¿¹Òȵ°°×øȱ·¦ÐԸβ¡(alpha1anti-trypsindeficiency-associatedliverdisease)ÊÇÒÅ´«ÐÔ1¿¹Òȵ°°×øȱ·¦ÒýÆðµÄ´úлÐÔ¸ÎÔ༲²¡£¬ÒÔ³£È¾É«ÌåÒþÐÔ·½Ê½(autosomalrecessivefashion)ÒÅ´«°éµÈÏÔÐÔ±í´ï(codominantexpression)¡£²é¿´Ïêϸ

ÐÔ±ð£ºÄÐÄêÁ䣺34Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÁõÏéÀñ

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺30Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÁõÏéÀñ

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÅ®ÄêÁ䣺1Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ˯Ãß ÌåÖØ

Ö¸µ¼Òâ¼û£ºÄãºÃºÜ¸ßÐËΪÄã½â´ð¸ÎÆ¢Ö×´óÒòʳ¹Ü¾²ÂöÇúÕÅÒýÆðµÄÉÏÏû»¯µÀ³öѪÐÂÉú¶ù¸ÎÔàÓÙµ¨ÈçÎÞºÃתÔò¿ÉÖð½¥·¢Õ¹³öÏÖ½øÐÐÐÔ¸ÎË𺦽øÕ¹Îª¸ÎÓ²»¯ÉõÖÁËÀÍö×£ÄãÔçÈÕ¿µ¸´

»Ø¸´Ò½Éú£ºËï¾´±ø

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺34Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÁõÏéÀñ

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺56Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÌÛÍ´

Ö¸µ¼Òâ¼û£º±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø±»¶¯

»Ø¸´Ò½Éú£ºÁõÏéÀñ

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺28Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö Òȵ°°×ø

Ö¸µ¼Òâ¼û£ºÄãºÃÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Í

»Ø¸´Ò½Éú£ºÀ±£

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺34Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÀ±£

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺53Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ Ìå¼ì ÌÛÍ´

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÀ±£

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺34Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÀ±£

¹²1¸ö»Ø´ð²é¿´>>

ÐÔ±ð£ºÄÐÄêÁ䣺30Ëê±êÇ©£º ¦Á1¿¹Òȵ°°×øȱ·¦ÐԸβ¡ ÉíÌå×´¿ö

Ö¸µ¼Òâ¼û£ºÄãºÃ±¾²¡ÉÐÎÞÓÐЧµÄÌØÊâÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½·¨»ù±¾°´¸ÎÓ²»¯µÄÒ»°ãÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«·½°¸½øÐÐÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óÈ«¸ÄÉÆÖ¢×´ºÍÊʵ±µÄÓªÑøÖ§³ÖΪ¼õÇᵨ֭ÓÙ»ýÐԸβ¡²¡Ç黼²¡Ó¤¶ùÓ¦¾¡¿ÉÄܸøÓèĸÈéÎ¹Ñø¸øÓèÖ¬ÈÜÐÔάÉúËØ¿ÉÊÔÓÃÐÜÈ¥Ñõµ¨ËáÕý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾´óȫҪ½äÑ̺Ͷžø

»Ø¸´Ò½Éú£ºÀ±£

¹²1¸ö»Ø´ð²é¿´>>

Ïà¹Ø±êÇ©
  • ¸¹Í´
  • ¶ñÐÄ
  • ¸¹Ðº
  • Å»ÍÂ
  • ±ãÃØ
  • ¸¹ÕÍ
  • θ¾µ
  • ʳÓû²»Õñ
  • ´òàÃ
  • θÕÍ
  • θʹ
  • θ²¡

Õý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾ÏÂÔØ

Ò©ÎïÐԸβ¡

Ò©ÎïÐԸβ¡

Ò©ÎïÐԸβ¡(druginducedliverdiseas[Ïêϸ]

µ¨Ö­ÐÔ¸ÎÓ²»¯

µ¨Ö­ÐÔ¸ÎÓ²»¯

µ¨Ö­ÐÔ¸ÎÓ²»¯ÏµÓÉÓÚ³¤ÆÚ¸ÎÄÚµ¨Ö­ÖÍÁô[Ïêϸ]

¸ÎÓ²»¯

¸ÎÓ²»¯

¸ÎÓ²»¯(hepaticsclerosis)ÊÇÁÙ´²³£¼û[Ïêϸ]

Õý°æ²¶ÓãÓÎÏ·(Öйú)app¹Ù·½ÏÂÔØ|Õý°æ²¶ÓãÓÎÏ·¹Ù·½ÍøÕ¾